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Invitrogen™ CLN5 Polyclonal Antibody

Rabbit Polyclonal Antibody
Marca: Invitrogen™ PA550936
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Descripción
CLN5 Polyclonal Antibody detects endogenous levels of CLN5 protein.
This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.[provided by RefSeq, Oct 2008].
Especificaciones
| CLN5 | |
| Polyclonal | |
| Unconjugated | |
| CLN5 | |
| A730075N08Rik; ceroid-lipofuscinosis; Ceroid-lipofuscinosis neuronal protein 5; ceroid-lipofuscinosis neuronal protein 5 homolog; Ceroid-lipofuscinosis neuronal protein 5 homolog, secreted form; Ceroid-lipofuscinosis neuronal protein 5, secreted form; ceroid-lipofuscinosis, neuronal 5; CLN5; NCL; Protein CLN5 | |
| Rabbit | |
| Antigen affinity chromatography | |
| RUO | |
| 1203, 211286, 306128 | |
| -20°C, Avoid Freeze/Thaw Cycles | |
| Liquid |
| ELISA, Western Blot | |
| 1 mg/mL | |
| PBS with 50% glycerol, 0.5% BSA and 0.02% sodium azide; pH 7.4 | |
| O75503, Q3UMW8 | |
| CLN5 | |
| Synthesized peptide derived from the Internal region of human CLN5. | |
| 100 μL | |
| Primary | |
| Human, Mouse, Rat | |
| Antibody | |
| IgG |
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