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Invitrogen™ ACADVL Polyclonal Antibody

Descripción
This antibody is tested in Peptide ELISA: antibody detection limit dilution 2,000.
The protein encoded by this gene is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. This acyl-Coenzyme A dehydrogenase is specific to long-chain and very-long-chain fatty acids. A deficiency in this gene product reduces myocardial fatty acid beta-oxidation and is associated with cardiomyopathy. Alternative splicing results in multiple transcript variants encoding different isoforms.
Especificaciones
Especificaciones
| Antígeno | ACADVL |
| Aplicaciones | Western Blot |
| Clasificación | Polyclonal |
| Concentración | 0.5 mg/mL |
| Conjugado | Unconjugated |
| Formulación | TBS with 0.5% BSA and 0.02% sodium azide; pH 7.3 |
| génica | ACADVL |
| N.º de referencia del gen | P49748 |
| Alias de gen | ACAD6; Acadvl; acyl-CoA dehydrogenase, very long chain; acyl-Coenzyme A dehydrogenase, very long chain; LCACD; MVLCAD; Very long chain Acyl-Coa dehydrogenase; very long-chain specific acyl-CoA dehydrogenase, mitochondrial; Vlcad; VLCAD very-long-chain acyl-CoA dehydrogenase |
| Símbolos de los genes | ACADVL |
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Título del producto
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